{"id":16522,"date":"2021-06-26T05:39:07","date_gmt":"2021-06-26T05:39:07","guid":{"rendered":"https:\/\/www.lifescienceart.com\/?p=16522"},"modified":"2021-06-26T05:39:07","modified_gmt":"2021-06-26T05:39:07","slug":"the-habsburg-jaw-a-genetic-legacy-of-inbreeding","status":"publish","type":"post","link":"https:\/\/www.lifescienceart.com\/tr\/science\/genetics\/the-habsburg-jaw-a-genetic-legacy-of-inbreeding\/","title":{"rendered":"Habsburg \u00c7enesi: Ensest Sonras\u0131 Genetik Miras"},"content":{"rendered":"<h2 class=\"wp-block-heading\">Habsburg \u00c7enesi: Ensestten Genetik Bir Miras<\/h2>\n\n<h2 class=\"wp-block-heading\">Habsburg Hanedan\u0131 ve Ensest<\/h2>\n\n<p>Habsburglar, 13. y\u00fczy\u0131ldan 19. y\u00fczy\u0131la kadar iktidarlar\u0131 Avrupa&#8217;n\u0131n b\u00fcy\u00fck bir k\u0131sm\u0131na yay\u0131lm\u0131\u015f Cermen-Avusturyal\u0131 bir y\u00f6netici hanedand\u0131. Bir\u00e7ok kraliyet ailesi gibi Habsburglar da iktidarlar\u0131n\u0131 peki\u015ftirmek i\u00e7in stratejik evlilikler yap\u0131yor ve genellikle yak\u0131n akrabalar\u0131yla evleniyorlard\u0131. Bu ensest uygulamas\u0131n\u0131n ailenin genetik yap\u0131s\u0131 ve fiziksel g\u00f6r\u00fcn\u00fcm\u00fc \u00fczerinde \u00f6nemli bir etkisi oldu.<\/p>\n\n<h2 class=\"wp-block-heading\">Habsburglar\u0131n Ay\u0131rt Edici \u00c7enesi<\/h2>\n\n<p>Habsburglar\u0131n en dikkat \u00e7ekici \u00f6zelliklerinden biri, \u00e7\u0131k\u0131nt\u0131l\u0131 alt \u00e7ene ve \u00e7\u00f6k\u00fck orta y\u00fcz ile karakterize edilen ay\u0131rt edici \u00e7eneleriydi. Mandibu\u0308ler prognatizm ve maksiller yetersizlik olarak bilinen bu y\u00fcz deformitesi, hanedanl\u0131\u011f\u0131n sonraki nesillerinde \u00f6zellikle belirgindi.<\/p>\n\n<h2 class=\"wp-block-heading\">Habsburg \u00c7enesinin Genetik Temeli<\/h2>\n\n<p>Son ara\u015ft\u0131rmalar, Habsburg \u00e7enesinin muhtemelen resesif bir gen taraf\u0131ndan olu\u015fturuldu\u011funu g\u00f6stermi\u015ftir. Resesif genler, yaln\u0131zca genin her iki kopyas\u0131 da ayn\u0131 oldu\u011funda etkilerini g\u00f6sterirler. Ensest, bireylerin ayn\u0131 resesif genin iki kopyas\u0131n\u0131 miras alma olas\u0131l\u0131\u011f\u0131n\u0131 art\u0131r\u0131r ve b\u00f6ylece resesif \u00f6zelli\u011fin ifade edilme olas\u0131l\u0131\u011f\u0131 artar.<\/p>\n\n<h2 class=\"wp-block-heading\">Ensest ile Habsburg \u00c7enesi Aras\u0131ndaki Korelasyon<\/h2>\n\n<p>Annals of Human Biology&#8217;de yay\u0131nlanan bir \u00e7al\u0131\u015fma, \u0130spanyol Habsburglar aras\u0131nda ensest d\u00fczeyi ile mandibuler prognatizmin ciddiyeti aras\u0131nda g\u00fc\u00e7l\u00fc bir korelasyon bulmu\u015ftur. Ara\u015ft\u0131rmac\u0131lar, 15 \u0130spanyol Habsburg&#8217;un portrelerini analiz ettiler ve \u00f6zde\u015f genlerinin oran\u0131n\u0131 \u00f6l\u00e7en ensest katsay\u0131lar\u0131n\u0131 belirlediler. Daha y\u00fcksek ensest katsay\u0131lar\u0131na sahip Habsburglar\u0131n daha belirgin Habsburg \u00e7enesi \u00f6zelliklerine sahip olma olas\u0131l\u0131\u011f\u0131n\u0131n daha y\u00fcksek oldu\u011funu buldular.<\/p>\n\n<h2 class=\"wp-block-heading\">Ensestin Habsburglar \u00dczerindeki Etkisi<\/h2>\n\n<p>Ay\u0131rt edici y\u00fcz \u00f6zelliklerinin yan\u0131 s\u0131ra ensestin Habsburglar \u00fczerinde ba\u015fka olumsuz sonu\u00e7lar\u0131 da olmu\u015ftur. \u00d6nceki ara\u015ft\u0131rmalar, ensestin Habsburg yavrular\u0131n\u0131n sa\u011f kalma \u015fans\u0131n\u0131 %18&#8217;e kadar azaltt\u0131\u011f\u0131n\u0131 g\u00f6stermi\u015ftir. Hanedanl\u0131\u011f\u0131n sonraki nesillerindeki y\u00fcksek d\u00fczeyde ensest, 18. y\u00fczy\u0131l\u0131n ba\u015flar\u0131nda Habsburg hanedan\u0131n\u0131n yok olmas\u0131na katk\u0131da bulunmu\u015f olabilir.<\/p>\n\n<h2 class=\"wp-block-heading\">Sonu\u00e7<\/h2>\n\n<p>Habsburg \u00e7enesi, ensestin genetik sonu\u00e7lar\u0131na dair \u00e7arp\u0131c\u0131 bir \u00f6rnektir. Bu y\u00fcz deformitesine, muhtemelen Habsburglar\u0131n akraba evlili\u011fi uygulamas\u0131 nedeniyle nesiller boyunca aktar\u0131lan resesif bir gen neden olmu\u015ftur. Ensest, Habsburglar \u00fczerinde sa\u011f kalma \u015fans\u0131n\u0131n azalmas\u0131 ve hanedanl\u0131\u011f\u0131n nihai olarak yok olmas\u0131 gibi ba\u015fka olumsuz etkilere de sahip olmu\u015ftur.<\/p>\n\n<h2 class=\"wp-block-heading\">Ek Bilgiler<\/h2>\n\n<ul class=\"wp-block-list\">\n<li><strong>Mandibuler prognatizm<\/strong>, \u00e7\u0131k\u0131nt\u0131l\u0131 alt \u00e7ene ile karakterize bir durumdur.<\/li>\n<li><strong>Makziller yetersizlik<\/strong>, \u00e7\u00f6k\u00fck orta y\u00fcz ile karakterize bir durumdur.<\/li>\n<li><strong>Dismorfik \u00f6zellikler<\/strong>, genetik bozukluklardan kaynaklanabilen anormal y\u00fcz \u00f6zellikleridir.<\/li>\n<li><strong>Ensest katsay\u0131s\u0131<\/strong>, bir bireyin genlerinin soy yoluyla \u00f6zde\u015f olma oran\u0131n\u0131n bir \u00f6l\u00e7\u00fcs\u00fcd\u00fcr.<\/li>\n<li><strong>Resesif gen<\/strong>, yaln\u0131zca genin her iki kopyas\u0131 da ayn\u0131 oldu\u011funda etkilerini g\u00f6steren bir gendir.<\/li>\n<\/ul>","protected":false},"excerpt":{"rendered":"<p>Habsburg \u00c7enesi: Ensestten Genetik Bir Miras Habsburg Hanedan\u0131 ve Ensest Habsburglar, 13. y\u00fczy\u0131ldan 19. y\u00fczy\u0131la kadar iktidarlar\u0131 Avrupa&#8217;n\u0131n b\u00fcy\u00fck bir k\u0131sm\u0131na yay\u0131lm\u0131\u015f Cermen-Avusturyal\u0131 bir y\u00f6netici hanedand\u0131. Bir\u00e7ok kraliyet ailesi gibi&hellip;<\/p>\n","protected":false},"author":6,"featured_media":0,"comment_status":"closed","ping_status":"","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[1628],"tags":[21879,188,21874,8741,21875,21878,21877,21880,21876],"class_list":["post-16522","post","type-post","status-publish","format-standard","hentry","category-genetics","tag-recessive-genes","tag-genetics","tag-habsburg-jaw","tag-inbreeding","tag-royal-families","tag-maxillary-deficiency","tag-mandibular-prognathism","tag-historical-portraits","tag-facial-deformities"],"_links":{"self":[{"href":"https:\/\/www.lifescienceart.com\/tr\/wp-json\/wp\/v2\/posts\/16522","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.lifescienceart.com\/tr\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.lifescienceart.com\/tr\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.lifescienceart.com\/tr\/wp-json\/wp\/v2\/users\/6"}],"replies":[{"embeddable":true,"href":"https:\/\/www.lifescienceart.com\/tr\/wp-json\/wp\/v2\/comments?post=16522"}],"version-history":[{"count":1,"href":"https:\/\/www.lifescienceart.com\/tr\/wp-json\/wp\/v2\/posts\/16522\/revisions"}],"predecessor-version":[{"id":16523,"href":"https:\/\/www.lifescienceart.com\/tr\/wp-json\/wp\/v2\/posts\/16522\/revisions\/16523"}],"wp:attachment":[{"href":"https:\/\/www.lifescienceart.com\/tr\/wp-json\/wp\/v2\/media?parent=16522"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.lifescienceart.com\/tr\/wp-json\/wp\/v2\/categories?post=16522"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.lifescienceart.com\/tr\/wp-json\/wp\/v2\/tags?post=16522"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}